HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS		QUICK SEARCH:   [advanced] Author: Keyword(s): Year:  Vol:  Page:

This Article Full Text Full Text (PDF) Alert me when this article is cited Alert me if a correction is posted Citation Map Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Add to Personal Folders Download to citation manager Author home page(s): Jonah Odim Hillel Laks Permission Requests Citing Articles Citing Articles via HighWire Citing Articles via Google Scholar Google Scholar Articles by Gupta, A. Articles by Laks, H. Search for Related Content PubMed PubMed Citation Articles by Gupta, A. Articles by Laks, H. Related Collections Congenital - cyanotic

J Thorac Cardiovasc Surg 2003;126:1746-1752
© 2003 The American Association for Thoracic Surgery

Surgery for congenital heart disease

Staged repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries: Experience with 104 patients

^a Division of Pediatric Cardiology, UCLA Medical Center, Los Angeles, Calif, USA
^b Division of Cardiothoracic Surgery, UCLA Medical Center, Los Angeles, Calif, USA

Received for publication January 2, 2003; revisions received May 8, 2003; accepted for publication June 18, 2003.

^* Address for reprints: Anuja Gupta, MD, 10621 Ashton Ave, Los Angeles, CA 90024, USA
doctoranuja{at}yahoo.com

OBJECTIVE: To determine the early and intermediate-term outcome of the staged repair used to treat children with pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries.

METHODS: We reviewed a retrospective case series of 104 patients with this complex lesion. Information was obtained from medical records and referring physicians.

RESULTS: Of the 104 patients treated with the staged repair, 58 achieved completion of anatomic repair. The 10-year mortality was 16.5%. In the patients with complete repair, the median right-to-left ventricle pressure ratio was 0.5. The overall surgical reoperation rate was 17%, and 15.5% of patients required postoperative interventional cardiac catheterization. In the multivariate analysis, the number of collateral vessels incorporated in the repair was found to be an independent risk factor for postoperative mortality and an elevated right-to-left ventricle pressure ratio after complete repair.

CONCLUSION: The staged repair can be successfully used to treat patients with pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. This method yields a relatively low mortality with good functional results.

This article has been cited by other articles:

				K. Januszewska, E. Malec, G. Juchem, I. Kaczmarek, R. Sodian, P. Uberfuhr, and B. Reichart Heart-lung transplantation in patients with pulmonary atresia and ventricular septal defect J. Thorac. Cardiovasc. Surg., September 1, 2009; 138(3): 738 - 743. [Abstract] [Full Text] [PDF]

				N. Ishibashi, T. Shin'oka, M. Ishiyama, T. Sakamoto, and H. Kurosawa Clinical results of staged repair with complete unifocalization for pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries Eur. J. Cardiothorac. Surg., August 1, 2007; 32(2): 202 - 208. [Abstract] [Full Text] [PDF]

				Y. Kaneko, H. Yoda, and K. Tsuchiya Airway Compression by Major Aortopulmonary Collaterals with 22q11 Deletion Asian Cardiovasc Thorac Ann, February 1, 2007; 15(1): e9 - e11. [Abstract] [Full Text] [PDF]

				E. Belli, L. Mace, M. Ly, P. Dervanian, E. Pineau, R. Roussin, E. Lebret, and A. Serraf Surgical management of pulmonary atresia with ventricular septal defect in late adolescence and adulthood Eur. J. Cardiothorac. Surg., February 1, 2007; 31(2): 236 - 241. [Abstract] [Full Text] [PDF]

				S Vesel, S Rollings, A Jones, N Callaghan, J Simpson, and G K Sharland Prenatally diagnosed pulmonary atresia with ventricular septal defect: echocardiography, genetics, associated anomalies and outcome Heart, October 1, 2006; 92(10): 1501 - 1505. [Abstract] [Full Text] [PDF]

				E. M. Ngan, I. M. Rebeyka, D. B. Ross, M. Hirji, J. F. Wolfaardt, R. Seelaus, A. Grosvenor, and M. L. Noga The rapid prototyping of anatomic models in pulmonary atresia J. Thorac. Cardiovasc. Surg., August 1, 2006; 132(2): 264 - 269. [Abstract] [Full Text] [PDF]

				K. M. Amark, T. Karamlou, A. O'Carroll, C. MacDonald, R. M. Freedom, S.-J. Yoo, W. G. Williams, G. S. Van Arsdell, C. A. Caldarone, and B. W. McCrindle Independent Factors Associated With Mortality, Reintervention, and Achievement of Complete Repair in Children With Pulmonary Atresia With Ventricular Septal Defect J. Am. Coll. Cardiol., April 4, 2006; 47(7): 1448 - 1456. [Abstract] [Full Text] [PDF]

				Y. d'Udekem, N. Alphonso, M. A. Norgaard, A. D. Cochrane, L. E. Grigg, J. L. Wilkinson, and C. P. Brizard Pulmonary atresia with ventricular septal defects and major aortopulmonary collateral arteries: Unifocalization brings no long-term benefits J. Thorac. Cardiovasc. Surg., December 1, 2005; 130(6): 1496 - 1502. [Abstract] [Full Text] [PDF]

				T. M Haga-Greco and K. S Niimi Construction of a pulmonary artery pump for unifocalization and repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collaterals Perfusion, March 1, 2005; 20(2): 109 - 113. [Abstract] [PDF]

				T. P. Graham Jr The year in congenital heart disease J. Am. Coll. Cardiol., June 2, 2004; 43(11): 2132 - 2141. [Full Text] [PDF]