HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS		QUICK SEARCH:   [advanced] Author: Keyword(s): Year:  Vol:  Page:

This Article Full Text Full Text (PDF) Alert me when this article is cited Alert me if a correction is posted Citation Map Services Email this article to a friend Similar articles in this journal Alert me to new issues of the journal Add to Personal Folders Download to citation manager Author home page(s): Takeshi Shinkawa Anastasios C. Polimenakos Jennifer C. Hirsch Eric J. Devaney Edward L. Bove Richard G. Ohye Permission Requests Citing Articles Citing Articles via HighWire Citing Articles via Google Scholar Google Scholar Articles by Shinkawa, T. Articles by Ohye, R. G. Search for Related Content PubMed Articles by Shinkawa, T. Articles by Ohye, R. G. Related Collections Congenital - cyanotic

J Thorac Cardiovasc Surg 2010;139:354-358
© 2010 The American Association for Thoracic Surgery

Congenital Heart Disease

Management and long-term outcome of neonatal Ebstein anomaly

^a Division of Pediatric Cardiovascular Surgery, Section of Cardiac Surgery, Department of Surgery, University of Michigan Medical School, Ann Arbor, Mich
^b Division of Pediatric Cardiology, Department of Pediatrics and Communicable Disease, University of Michigan Medical School, Ann Arbor, Mich

Received for publication January 9, 2009; revisions received April 8, 2009; accepted for publication July 23, 2009.

^_* Address for reprints: Richard G. Ohye, MD, 5144 CVC/SPC 5864, 1500 East Medical Center Dr, Ann Arbor, MI 48109-5864. (Email: ohye{at}umich.edu).

Objective: The objective of this study was to review the long-term results of symptomatic patients with Ebstein anomaly in the neonatal period.

Methods: The medical records of 40 neonates with a diagnosis of Ebstein anomaly who were admitted to our institution between January 1988 and June 2008 were retrospectively reviewed. Primary outcomes studied included patient survival and need for reintervention.

Results: No early intervention was required in 16 of the 40 patients with a hospital survival of 94% (15/16) and no late mortality. The remaining 24 patients underwent surgical intervention in the neonatal period. A shunt alone was performed in 9 patients with an actuarial survival of 88.9% at 1 year and 76.2% at 5 and 10 years. For the patients undergoing intervention on the tricuspid valve, survival estimates for the 11 patients with a right ventricular exclusion procedure were 63.6% at 1, 5, and 10 years and 47.7% at 15 years compared with 25.0% at 1, 5, and 10 years for the 4 patients with tricuspid valve repair. All long-term survivors were in New York Heart Association class I or II, and only 1 patient required antiarrhythmic medication.

Conclusion: Symptomatic neonates with Ebstein anomaly requiring no intervention or shunting alone have good long-term survival. For patients needing intervention on the tricuspid valve, overall survival is lower. For these patients, right ventricular exclusion may be superior to tricuspid valve repair.

This article has been cited by other articles:

				A. Muralidaran, R. W. Kim, G. S. Kopf, N. P. Pietris, B. P. Weeks, V. A. Starnes, and T. Shinoka Modified Starnes Procedure in a Neonate With Severe Tricuspid Regurgitation Ann. Thorac. Surg., February 1, 2012; 93(2): 658 - 659. [Abstract] [Full Text] [PDF]

				C. J. Knott-Craig, S. P. Goldberg, J. A. Ballweg, and U. S. Boston Surgical Decision Making in Neonatal Ebstein's Anomaly: An Algorithmic Approach Based on 48 Consecutive Neonates World Journal for Pediatric and Congenital Heart Surgery, January 1, 2012; 3(1): 16 - 20. [Abstract] [Full Text] [PDF]

				T. Kawabata, S. Kasahara, S. Arai, and S. Sano Right ventricular exclusion for a neonatal patient with Ebstein anomaly: A free wall resection of the right ventricle J. Thorac. Cardiovasc. Surg., December 1, 2011; 142(6): 1582 - 1584. [Full Text] [PDF]

				S. P. Goldberg, R. C. Jones, U. S. Boston, L. M. Haddad, G. T. Wetzel, T. K. Chin, and C. J. Knott-Craig Current Trends in the Management of Neonates With Ebstein's Anomaly World Journal for Pediatric and Congenital Heart Surgery, October 1, 2011; 2(4): 554 - 557. [Abstract] [Full Text] [PDF]

				U. S. Boston, S. P. Goldberg, K. E. Ward, E. D. Overholt, T. Spentzas, T. K. Chin, and C. J. Knott-Craig Complete repair of Ebstein anomaly in neonates and young infants: A 16-year follow-up J. Thorac. Cardiovasc. Surg., May 1, 2011; 141(5): 1163 - 1169. [Abstract] [Full Text] [PDF]

				T. P. Graham Jr The Year in Congenital Heart Disease J. Am. Coll. Cardiol., January 11, 2011; 57(2): 210 - 218. [Full Text] [PDF]