HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS		QUICK SEARCH:   [advanced] Author: Keyword(s): Year:  Vol:  Page:

This Article Alert me when this article is cited Alert me if a correction is posted Citation Map Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Add to Personal Folders Download to citation manager Permission Requests Citing Articles Citing Articles via HighWire Citing Articles via Google Scholar Google Scholar Articles by Alboliras, E. T. Articles by Driscoll, D. J. Search for Related Content PubMed PubMed Citation Articles by Alboliras, E. T. Articles by Driscoll, D. J.

The Journal of Thoracic and Cardiovascular Surgery, Vol 93, 454-464, Copyright © 1987 by The American Association for Thoracic Surgery and The Western Thoracic Surgical Association

ARTICLES

Definitive operation for pulmonary atresia with intact ventricular septum. Results in twenty patients

ET Alboliras, PR Julsrud, GK Danielson, FJ Puga, HV Schaff, DC McGoon, DJ Hagler, WD Edwards and DJ Driscoll

Definitive operation was performed on 20 patients (aged 25 to 178 months) with pulmonary atresia and intact ventricular septum. All patients had one or more prior preliminary palliative procedures. Right ventricular outflow tract reconstruction with atrial septal defect closure and shunt removal was done on 10 patients. Tricuspid annular circumference was at least 70% of normal in seven patients and between 55% and 70% in three patients. Two patients died during hospitalization. The eight surviving patients were asymptomatic 3 to 145 months after operation. The modified Fontan operation was performed on 10 patients. None of these patients had a tricuspid annular circumference greater than 70% of normal; the circumference was less than 55% in nine patients and between 55% and 70% in one patient. One patient died during hospitalization and one died later. Follow-up 6 to 48 months after operation showed that six patients were in the New York Heart Association Class I and two were in Class II. After effective preliminary palliation of pulmonary atresia with intact ventricular septum, definitive operation can be done with an operative risk of 15% (three of 20 patients) and excellent late results. Right ventricular outflow tract reconstruction can be done as a complete repair for patients who have adequate tricuspid annular size. The modified Fontan operation is the only option for definitive repair when the tricuspid anulus is severely hypoplastic.

This article has been cited by other articles:

				T. Sluysmans and S. D. Colan Theoretical and empirical derivation of cardiovascular allometric relationships in children J Appl Physiol, August 1, 2005; 99(2): 445 - 457. [Abstract] [Full Text] [PDF]

				N. Yoshimura, M. Yamaguchi, H. Ohashi, Y. Oshima, S. Oka, M. Yoshida, H. Murakami, and T. Tei Pulmonary atresia with intact ventricular septum: Strategy based on right ventricular morphology J. Thorac. Cardiovasc. Surg., November 1, 2003; 126(5): 1417 - 1426. [Abstract] [Full Text] [PDF]

				H. Shimpo, H. Hayakawa, Y. Miyake, S. Takabayashi, and I. Yada Strategy for pulmonary atresia and intact ventricular septum Ann. Thorac. Surg., July 1, 2000; 70(1): 287 - 289. [Abstract] [Full Text] [PDF]

				M. Alwi, K. Geetha, A. A. Bilkis, M. K. Lim, S. Hasri, A. L. Haifa, A. Sallehudin, and R. Zambahari Pulmonary atresia with intact ventricular septum percutaneous radiofrequency-assisted valvotomy and balloon dilation versus surgical valvotomy and blalock taussig shunt J. Am. Coll. Cardiol., February 1, 2000; 35(2): 468 - 476. [Abstract] [Full Text] [PDF]

				C. Ovaert, S. A. Qureshi, E. Rosenthal, E. J. Baker, and M. Tynan Growth of the right ventricle after successful transcatheterpulmonary valvotomy in neonates and infants with pulmonary atresia and intactventricular septum J. Thorac. Cardiovasc. Surg., May 1, 1998; 115(5): 1055 - 1059. [Abstract] [Full Text] [PDF]

				C. J. Knott-Craig, G. K. Danielson, H. V. Schaff, F. J. Puga, A. L. Weaver, and D. D. Driscoll The modified fontan operationAn analysis of risk factors for early postoperative death or takedown in 702 consecutive patients from one institution J. Thorac. Cardiovasc. Surg., June 1, 1995; 109(6): 1237 - 1243. [Abstract] [Full Text]

				C. Bull, M. Kostelka, K. Sorensen, and M. de Leval Outcome measures for the neonatal management of pulmonary atresia with intact ventricular septum J. Thorac. Cardiovasc. Surg., February 1, 1994; 107(2): 359 - 366. [Abstract] [Full Text]

				J. G. Coles, R. M. Freedom, N. E. Lightfoot, H. K. Dasmahapatra, W. G. Williams, G. A. Trusler, and P. E. Burrows Long-term results in neonates with pulmonary atresia and intact ventricular septum Ann. Thorac. Surg., February 1, 1989; 47(2): 213 - 217. [Abstract] [PDF]