HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS		QUICK SEARCH:   [advanced] Author: Keyword(s): Year:  Vol:  Page:

This Article Full Text Full Text (PDF) Alert me when this article is cited Alert me if a correction is posted Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Add to Personal Folders Download to citation manager Author home page(s): Shunei Kyo Yuji Yokote Permission Requests Citing Articles Citing Articles via Google Scholar Google Scholar Articles by Senzaki, H. Articles by Yokote, Y. Search for Related Content PubMed PubMed Citation Articles by Senzaki, H. Articles by Yokote, Y. Related Collections Congenital - acyanotic

J Thorac Cardiovasc Surg 2003;126:1645-1647
© 2003 The American Association for Thoracic Surgery

Brief communications

Anomalous origin of the left coronary artery from the main pulmonary artery associated with Berry syndrome

^a Department of Pediatric Cardiology and Cardiovascular Surgery, Saitama Medical School Hospital, Saitama, Japan

Received for publication January 14, 2003; accepted for publication June 18, 2003.

^* Address for reprints: Hideaki Senzaki, MD, Department of Pediatric Cardiology, Saitama Heart Institute, Saitama Medical School Hospital, 38 Morohongo, Moroyama, Saitama, 350-0495 Japan
hsenzaki@saitama-med.ac.jp

The first 20% of the full text of this article appears below.

Berry syndrome, which consists of distal aortopulmonary septal defect (APSD), aortic origin of the right pulmonary artery, interrupted aortic arch, intact ventricular septum, and patent ductus arteriosus, is an extremely uncommon congenital cardiac malformation, with only 25 cases having been reported since the first report in 1982.^1,2 Here we report the first case of Berry syndrome complicated by anomalous origin of the left coronary artery from the main pulmonary artery. The possibility of coronary anomaly should be seriously considered in all cases of Berry syndrome.

Clinical summary

A 2-day-old male infant weighing 3.2 kg was referred to our hospital because of congestive heart failure. Electrocardiography showed right ventricular hypertrophy, and chest radiography showed cardiomegaly with increased pulmonary vascular markings. Echocardiography revealed a type A interrupted aortic arch, a confluent APSD, aortic origin of the right pulmonary artery, an intact ventricular septum, and a patent ductus arteriosus. Cardiac catheterization and angiography confirmed the above diagnosis (Figure 1). However, at that point, we had not detected anomalous origin of the left coronary artery from the main pulmonary artery. At 6 days of age, the patient underwent surgical intervention for total repair through a median sternotomy. An end-to-side anastomosis of the descending aorta to the undersurface of the aortic arch was performed during circulatory arrest. Low-flow bypass was resumed, and during cardioplegic . . . [Full Text of this Article]